Diagnosis of ADPKD by imaging and/or genetic testing
GFR ≥ 25 mg/dl
Patients at risk for rapid progression of ADPKD: Mayo Class 1C-1E along with any other high risk features including early decline in GFR, hypertension onset ≤ 35 years of age, urologic events ≤ 35 years of age, PKD 1 truncating mutation and PROPKD score of 4 or higher as determined by the treating physician
No changes of medications within the last three months.
Able to comply with dietary intervention
Ability to sign informed consent
You may not be if
Patients currently being treated with Tolvaptan
Diagnosed with diabetes.
Pregnancy
Contraindications to MRI
Ketogenic diet within the last three months
Severe kidney disease with GFR \< 25 mg/dl
Unable to purchase food for the diet intervention
Gastrointestinal disorders that will interfere with diet intervention
Chronic alcohol or drug abuse
Clareo Health | Well-Formulated Ketogenic Diet Polycystic Kidney Disease
